Sickle Cell Anemia

Sickle Cell Anemia

Sickle Cell Anemia

Sickle Cell Anemia (SCA)

SCD Polymerization of Hgb

Polymerization

Polymerization leads to . . .

Manifestations

Clinical Presentation

The Lung in SCA

Pneumonia

Pneumonia

Slide 13

Acute Chest Syndrome (ACS)

Acute Chest Syndrome (ACS)

ACS: etiologies

ACS: Radiology

ACS: Radiology

ACS: Radiology

ACS: progression

Chronic Pulmonary Disease

 Chronic Pulmonary Disease

The Skeletal System in SCA

Marrow Expansion

Marrow Expansion

Marrow Expansion

Marrow Expansion

Marrow Expansion

Slide 29

Infarction

Infarction: Imaging

 Infarction: Imaging

"Epiphyseal Infarction"

Subchondral Infarction

Bone Infarction

Dactylitis
Hand-Foot Syndrome

Dactylitis

Dactylitis

Osteomyelitis

Osteomyelitis

Osteomyelitis

The Brain in SCA

Stroke

SCD Cerebral Infarction

Stroke Screening
Transcranial Doppler (TCD)

Screening with TCD

Stroke Prevention

The Spleen in SCA

Infarction

Splenic Infarction

Splenic Infarction

Sequestration

Sequestration

Sequestration

Sequestration

The Kidney

Slide 57

Slide 58

Other Complications

Gall Stones

Gall Stones

Slide 62

Treatment

Prognosis